[Primary familial erythromelalgia. A case report].
Bouyahyaoui Y, Meziane M, Hanaae Z, Mikou O, Mernissi FZ, et al.
Archives de pediatrie : organe officiel de la Societe francaise de pediatrie •
Erythromelalgia is a rare disease whose etiology is poorly understood. It is characterized by paroxysmal attacks of erythema, pain, and warmth of the extremities and can be primary or secondary. We report a case of primary familial erythromelalgia and stress the difficulties in its therapeutic management. We provide a brief update on the pathophysiology and treatment of primary erythromelalgia.